Non-compaction: a distinct cardiomyopathy or non-specific morphological trait?
نویسندگان
چکیده
منابع مشابه
Right Ventricular Non-Compaction Cardiomyopathy in Children: Brief Review Literature
Right ventricular non-compaction cardiomyopathy (RVNC) is a genetic heterogeneous cardiomyopathy. Despite the increasing number of RVNC cases, the classification and natural history of this disorder are not completely clear. Also, because the pathogenic non-compaction cannot be easily differentiated from normal trabeculations, it is usually hard to accurately measure the prevalence of RV ...
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Left ventricular non-compaction (spongy myocardium) is one of the most misclassified cardiomyopathies. It is characterised by an excessively prominent trabecular meshwork of myocardium and deep intertrabecular myocardium due to an arrest in the compaction process of the myocardial fibres. It could be isolated i.e. without any other structural heart defects or associated with congenital heart de...
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Non-compaction of the left ventricle is an extremely rare cardiomyopathy resulting from a defective morphogenesis of the endomyocardium. It results in an architecturally aberrant ventricular wall consisting of two layers: a compacted layer and a loose interwoven meshwork with prominent trabeculae and deep intertrabecular recesses that communicate with the left ventricular cavity. This report de...
متن کاملIsolated non-compaction cardiomyopathy.
BACKGROUND Isolated non-compaction cardiomyopathy (NCCM) was first described in 1984. This disorder, a primary genetic cardiomyopathy, is now attracting increased attention. METHOD The current state of the epidemiology, pathogenesis, pathophysiology, clinical features, diagnosis, treatment, and prognosis of NCCM are discussed on the basis of a review of selected literature as well as the auth...
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Hypertrophic cardiomyopathy (HCM) is a familial cardiac disease caused by mutations in one or more of 12 genes encoding protein components of the cardiac sarcomere. The disease is transmitted with an autosomal dominant trait and a variable penetrance. The phenotypic features of HCM may develop at any age from infancy to adulthood, and are characterized by a great heterogeneity in the extent, ma...
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ژورنال
عنوان ژورنال: European Heart Journal
سال: 2008
ISSN: 0195-668X,1522-9645
DOI: 10.1093/eurheartj/ehn029